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Cardiac Arrhythmias in Adults with Congenital Heart Disease, An Issue of Cardiac Electrophysiology Clinics, E-Book

Cardiac Arrhythmias in Adults with Congenital Heart Disease, An Issue of Cardiac Electrophysiology Clinics, E-Book

Balaji Seshadri | Ravi Mandapati | Kalyanam Shivkumar

(2017)

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Book Details

Abstract

This issue of Cardiac Electrophysiology Clinics, edited by Drs. Ravi Mandapati, Kalyanam Shivkumar, and Seshadri Balaji, will cover the latest in Cardiac Arrhythmias in Adults with Congenital Heart Disease. Topics covered in this issue include, but are not limited to Brady arrhythmia; Supraventricular Tachycardia in Adult Congenital Heart Disease; Atrial defects, Ebsteins; Drug therapy; Devices; and Surgery.

Table of Contents

Section Title Page Action Price
Front Cover Cover
Cardiac Arrhythmias inAdults with CongenitalHeart Disease\r i
Copyright\r ii
Contributors iii
CONSULTING EDITORS iii
EDITORS iii
AUTHORS iii
Contents vii
Foreword vii
Preface vii
Mechanisms, Diagnosis and Clinical Aspects vii
Introduction to the Congenital Heart Defects: Anatomy of the Conduction System167 vii
Bradyarrhythmias in Congenital Heart Disease vii
Supraventricular Tachycardia in Adult Congenital Heart Disease: Mechanisms, Diagnosis, and Clinical Aspects vii
Ventricular Arrhythmias in Adult Congenital Heart Disease: Mechanisms, Diagnosis, and Clinical Aspects viii
Sudden Cardiac Death in Adult Congenital Heart Disease viii
Specific Congenital Heart Defects: Clinical Aspects and Ablation viii
Arrhythmias in Patients with Atrial Defects235 viii
Ebstein Anomaly viii
Arrhythmias Following the Mustard and Senning Operations for Dextro-Transposition of the Great Arteries: Clinical Aspects a ... ix
Development of Tachyarrhythmias Late After the Fontan Procedure: The Role of Ablative Therapy ix
Clinical Aspects and Ablation of Ventricular Arrhythmias in Tetralogy of Fallot ix
Management ix
Drug Therapy in Adult Congenital Heart Disease295 ix
Catheter Ablation: General Principles and Advances x
Cardiac Arrhythmias in Adults with Congenital Heart Disease: Pacemakers, Implantable Cardiac Defibrillators, and Cardiac Re ... x
Arrhythmia Surgery for Adults with Congenital Heart Disease x
CARDIAC ELECTROPHYSIOLOGY CLINICS\r xi
FORTHCOMING ISSUES xi
September 2017 xi
December 2017 xi
March 2018 xi
RECENT ISSUES xi
March 2017 xi
December 2016 xi
September 2016 xi
Foreword xiii
Preface\r xv
Cardiac Arrhythmias in Adults with Congenital Heart Disease\r xv
Introduction to the Congenital Heart Defects 167
Key points 167
INTRODUCTION 167
SIMPLE DEFECTS 168
Atrial Septal Defect 168
Ventricular Septal Defect 168
MODERATELY COMPLEX DEFECTS 168
Atrioventricular Septal Defect 168
Congenitally Corrected Transposition of the Great Arteries 169
Tetralogy of Fallot 170
COMPLEX DEFECTS 171
Tricuspid Atresia 171
Double Inlet Left Ventricle 172
Heterotaxy Syndromes 172
SUMMARY 173
REFERENCES 173
Bradyarrhythmias in Congenital Heart Disease 177
Key points 177
INTRODUCTION 177
THE SPECTRUM OF BRADYARRHYTHMIAS IN CONGENITAL HEART DISEASE 178
Unrepaired Congenital Heart Disease 178
Heterotaxy syndromes 178
Atrioventricular septal defects 179
Congenitally corrected transposition of the great arteries 180
Other congenital heart disease defects 180
Repaired Congenital Heart Disease 180
Postsurgical sinus node dysfunction 180
Postsurgical complete heart block 181
CLINICAL SEQUELAE AND TREATMENT OF BRADYARRHYTHMIAS IN ADULT CONGENITAL HEART DISEASE 182
SUMMARY 186
REFERENCES 186
Supraventricular Tachycardia in Adult Congenital Heart Disease 189
Key points 189
INTRODUCTION 189
GENERAL MECHANISMS OF SUPRAVENTRICULAR TACHYCARDIA 190
CHALLENGES IN THE DIAGNOSIS AND MANAGEMENT OF SUPRAVENTRICULAR TACHYCARDIA IN ADULTS WITH CONGENITAL HEART DISEASE 190
Atrioventricular Nodal Reentrant Tachycardia 191
Pathophysiology 191
Diagnosis 192
Management 192
Accessory-Pathway Mediated Tachycardia 195
Pathophysiology 195
Diagnosis 195
Management 198
Twin Atrioventricular Nodes 199
Pathophysiology 199
Diagnosis 200
Management 201
Intra-atrial Reentry Tachycardia 201
Pathophysiology 201
Diagnosis 202
Management 202
Atrial Fibrillation 204
Pathophysiology 204
Diagnosis 204
Management 205
Focal Atrial Tachycardia 205
Pathophysiology 206
Diagnosis 206
Management 207
Junctional Tachycardia 207
Pathophysiology 207
Diagnosis 207
Management 208
REFERENCES 208
Ventricular Arrhythmias in Adult Congenital Heart Disease 213
Key points 213
INTRODUCTION 213
PATHOPHYSIOLOGY OF VENTRICULAR ARRHYTHMIAS 214
ELECTROCARDIOGRAPHIC DIAGNOSIS OF VENTRICULAR TACHYCARDIA 214
VENTRICULAR ARRHYTHMIAS IN TETRALOGY OF FALLOT 215
Pathophysiology and Mechanisms for Ventricular Arrhythmias 215
Risk Factors for Ventricular Arrhythmias and Sudden Cardiac Death 215
TRANSPOSITION OF THE GREAT ARTERIES 216
Pathophysiology and Mechanisms for Ventricular Arrhythmias 216
Risk Factors for Ventricular Arrhythmias and Sudden Cardiac Death 217
THE SINGLE VENTRICLE 218
Pathophysiology and Mechanisms for Ventricular Arrhythmias 218
Risk Factors for Ventricular Arrhythmias and Sudden Cardiac Death 218
EBSTEIN ANOMALY 219
Sudden Cardiac Death in Adult Congenital Heart Disease 225
Key points 225
INTRODUCTION 225
SCOPE OF THE PROBLEM 226
MECHANISMS OF SUDDEN CARDIAC DEATH 226
SECONDARY PREVENTION OF SUDDEN CARDIAC DEATH 226
PRIMARY PREVENTION OF SUDDEN CARDIAC DEATH 228
Challenges in Risk Stratification 228
Tetralogy of Fallot 230
Systemic Left Ventricle with Biventricular Physiology 231
Systemic Right Ventricle 231
Univentricular Hearts 232
SUMMARY 232
REFERENCES 233
Arrhythmias in Patients with Atrial Defects 235
Key points 235
INTRODUCTION 235
ATRIAL SEPTAL DEFECTS AND PATENT FORAMEN OVALES: PATHOLOGY AND GENERAL MANAGEMENT 235
ELECTROCARDIOGRAPHIC CHANGES SEEN WITH ATRIAL SEPTAL DEFECTS 235
ATRIAL ARRHYTHMIAS WITH ATRIAL SEPTAL DEFECTS/PATENT FORAMEN OVALES 236
PATHOPHYSIOLOGY OF ARRHYTHMIAS WITH ATRIAL SEPTAL DEFECTS 236
Before Closure/Repair of an Atrial Septal Defect 236
After/Post Device/Surgical Closure 237
Local irritation 237
Atriotomy scar after surgical closure 237
Presence of occlusion device 237
A Mechanism Independent of Atrial Septal Defect? 238
MANAGEMENT OF ARRHYTHMIAS 238
Confirming the Mechanism of Arrhythmia 238
Mapping the Arrhythmia 238
Ablation 239
Ablation of Left Atrial Arrhythmias in Patients After Atrial Septal Defect Repair/Closure: Issues with Transseptal Puncture 241
SUMMARY 243
REFERENCES 243
Ebstein Anomaly 245
Key points 245
INTRODUCTION 245
PRACTICAL CONSIDERATIONS IN ELECTROPHYSIOLOGICAL PROCEDURES IN EBSTEIN ANOMALY 246
ARRHYTHMIA MECHANISMS 246
Accessory Pathway–Mediated Tachycardia 246
Atrial Flutter and Other Atrial Arrhythmias 248
Ventricular Tachycardia 250
Sudden Cardiac Death 250
Preoperative Assessment and Arrhythmia Surgery 251
SUMMARY 253
REFERENCES 253
Arrhythmias Following the Mustard and Senning Operations for Dextro-Transposition of the Great Arteries 255
Key points 255
INTRODUCTION 255
SURGICAL ANATOMY 256
Senning Operation 256
Mustard Operation 256
ARRHYTHMIA BURDEN 257
Sinoatrial Node Dysfunction 257
Intra-Atrial Reentry Tachycardia and Other Forms of Supraventricular Tachycardia 258
Sudden Cardiac Death 259
NONABLATIVE THERAPIES 260
Antiarrhythmic Drug Therapies 260
Antitachycardia Pacing for Atrial Tachyarrhythmias 260
Other Nonablative Therapies: Bradycardia Pacing, Implantable Cardioverter-Defibrillators, Cardiac Resynchronization Therapy 260
CATHETER ABLATION STRATEGIES 261
Electrophysiological Anatomy 261
Preparation 263
Anatomic variations 263
Hemodynamic fragility 263
Vascular access 263
Electrophysiologic substrates/data acquisition 263
Ablation of Intra-Atrial Reentry Tachycardia 264
Focal Atrial Tachycardia 267
Atrioventricular Nodal Reentrant Tachycardia 268
SUMMARY 269
REFERENCES 269
Development of Tachyarrhythmias Late After the Fontan Procedure 273
Key points 273
INTRODUCTION 273
INDICATIONS FOR THE FONTAN PROCEDURE 273
DIFFERENT TYPES OF FONTAN PROCEDURES 274
PATHOPHYSIOLOGY OF SUPRAVENTRICULAR TACHYARRHYTHMIAS 274
MACRO-REENTRANT TACHYCARDIAS 274
FOCAL ATRIAL TACHYCARDIAS 275
ATRIAL FIBRILLATION 276
COEXISTENT ATRIAL FIBRILLATION AND ATRIAL TACHYARRHYTHMIA 276
THERAPY FOR ATRIAL TACHYARRHYTHMIAS 277
ELECTRO-ANATOMIC ACTIVATION MAPPING 277
ELECTRO-ANATOMIC VOLTAGE MAPPING 278
OUTCOME OF ABLATIVE THERAPY 279
SURGICAL MAZE IN FONTAN PATIENTS 281
VENTRICULAR TACHYARRHYTHMIAS 282
SUMMARY 282
ACKNOWLEDGMENTS 282
REFERENCES 283
Clinical Aspects and Ablation of Ventricular Arrhythmias in Tetralogy of Fallot 285
Key points 285
INTRODUCTION 285
VENTRICULAR ARRHYTHMIAS 285
RISK STRATIFICATION AND VENTRICULAR ARRHYTHMIA SUBSTRATES 286
SUBSTRATE FOR MONOMORPHIC VENTRICULAR TACHYCARDIA IN REPAIRED TETRALOGY OF FALLOT 286
CONTRIBUTION OF 3-DIMENSIONAL ELECTROANATOMICAL MAPPING FOR SUBSTRATE IDENTIFICATION AND RISK STRATIFICATION 287
VENTRICULAR TACHYCARDIA ABLATION: STRATEGIES, END POINTS, AND OUTCOME 289
PROCEDURAL FAILURE 292
SUMMARY 293
REFERENCES 293
Drug Therapy in Adult Congenital Heart Disease 295
Key points 295
INTRODUCTION 295
ANTIARRHYTHMIC DRUGS 296
CLASS I ANTIARRHYTHMIC AGENTS 296
Class 1 Agents in Patients with Congenital Heart Disease 296
Class 1A antiarrhythmics 296
Quinidine 296
Procainamide 296
Disopyramide 298
Class 1B agents 298
Lidocaine 298
Mexiletine 298
Mexiletine for ventricular arrhythmias in patients with congenital heart disease 298
Phenytoin 298
Class 1C agents 298
Flecainide 299
Propafenone 299
CLASS II AGENTS 299
Selectivity 299
Lipophilic Versus Hydrophilic Properties 299
Intrinsic Sympathomimetic Activity 299
Half-life 300
CLASS III AGENTS 300
Amiodarone 300
Amiodarone for supraventricular arrhythmias in patients with congenital heart disease 301
Amiodarone for ventricular arrhythmias in patients with congenital heart disease 301
Sotalol and Dofetilide 301
Sotalol for supraventricular arrhythmias in congenital heart disease 301
Sotalol for ventricular arrhythmias in congenital heart disease 301
Dofetilide for supraventricular arrhythmias in congenital heart disease 301
Dronedarone 303
Dronedarone for supraventricular arrhythmias in congenital heart disease 303
Ibutilide 303
Ibutilide for supraventricular arrhythmias in congenital heart disease 303
CLASS VI ANTIARRHYTHMICS 304
Miscellaneous Antiarrhythmics 304
Ranolazine 304
Adenosine 304
Digoxin 304
Magnesium 304
SPECIAL CONSIDERATIONS FOR ANTIARRHYTHMICS IN PATIENTS WITH ADULT CONGENITAL HEART DISEASE 305
Use of Class 1C Antiarrhythmics in Patients with Congenital Heart Disease 305
Use of Sotalol in Patients with Congenital Heart Disease 305
Anticoagulants 305
Which arrhythmia warrants anticoagulation? 305
Who needs anticoagulation? 305
Which medication? 307
What about anticoagulation in the pericardioversion period? 307
REFERENCES 307
Catheter Ablation 311
Key points 311
INTRODUCTION 311
GENERAL PREPARATION OF PATIENTS WITH CONGENITAL HEART DISEASE PRESENTING WITH ARRHYTHMIAS 311
Standard Imaging Studies 312
PREPARATION OF THE ABLATION PROCEDURE 312
Detailed Knowledge of Individual Anatomy 312
Review of Surgical Procedure Note 312
ADVANCED TECHNIQUES 312
Three-Dimensional Image Reconstruction 312
Three-Dimensional Imaging for Procedural Planning 313
Vascular Access: Femoral 314
Vascular Access: Alternative 314
INTRAPROCEDURAL CONSIDERATIONS 314
Dedicated Anesthetic Monitoring 314
Three-Dimensional Electroanatomic Mapping 314
Multielectrode High-Resolution Mapping 314
Simultaneous Mapping System 315
Catheter Ablation Techniques 315
Remote Navigation by Magnetic Navigation 315
SUMMARY 316
REFERENCES 316
Cardiac Arrhythmias in Adults with Congenital Heart Disease 319
Key points 319
INTRODUCTION 319
PACEMAKER IMPLANTATION 320
Pacing in Specific Anatomic Variants 321
IMPLANTABLE CARDIAC DEFIBRILLATOR IMPLANTATION 322
CARDIAC RESYNCHRONIZATION THERAPY VIA BIVENTRICULAR OR MULTISITE PACING 323
Cardiac Resynchronization Therapy for the Systemic Left Ventricle 324
Cardiac Resynchronization Therapy for the Subpulmonary Right Ventricle 324
Cardiac Resynchronization Therapy for the Systemic Right Ventricle 324
Cardiac Resynchronization Therapy for the Single Ventricle 325
SPECIAL SITUATIONS: LEAD EXTRACTION, VENOUS OCCLUSIONS, AND INTRACARDIAC SHUNTS 325
SUMMARY 326
REFERENCES 326
Arrhythmia Surgery for Adults with Congenital Heart Disease 329
Key points 329
INTRODUCTION 329
STRUCTURAL CONGENITAL HEART DISEASE AND ARRHYTHMIAS 330
Mechanisms of Supraventricular Tachycardia 330
Ventricular Tachycardia 331
ARRHYTHMIA SURGERY 332
Recommendations for Arrhythmia Surgery 333
ARRHYTHMIA SURGERY TECHNIQUES 333
ATRIAL REENTRY TACHYCARDIA AND ATRIAL FLUTTER 333
ATRIAL FIBRILLATION 336
PROPHYLACTIC ARRHYTHMIA SURGERY 336
REFERENCES 337