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Congenital Heart Disease in Adults E-Book

Congenital Heart Disease in Adults E-Book

Joseph K. Perloff | John S. Child | Jamil Aboulhosn

(2008)

Additional Information

Book Details

Abstract

Dr. Perloff, the founding father of the field of adult congenital heart disease, presents a decade’s worth of research and clinical data in the completely redefined 3rd edition to bring you the most current information. With advances in diagnosis and treatment in children, more and more of those with CHD survive well into adulthood. Expert contributors in various fields offer a multi-disciplinary, multi-system approach to treatment so you get comprehensive coverage on all aspects of the subspecialty, including basic unoperated malformations, medical and surgical perspectives, postoperative residue, and sequelae. As someone who treats these patients, you need to be ready to provide the continual care they require.

  • Conveys a multidisciplinary, multi-system approach to the lifelong care of adult CHD patients to put treatment in a broader context.
  • Presents information in a consistent, logical style so the information you need is easy to find and apply.
  • Supplements the text with 600 clear conceptual illustrations to clarify difficult concepts.
  • Features completely rewritten chapters to include the latest developments in the field—such as major advances in surgical and interventional techniques—and the various needs of patients with adult CHD.
  • Incorporates recently published trials such as those involving cyanotic CHD and atherogenesis, coronary microcirculation, and pathogenesis of thrombocytopenia to supplement the chapter on cyanotic CHD.
  • Emphasizes advances in imaging in a new section—edited by an expert—that covers echocardiography as well as specialized imaging techniques.
  • Illustrates the full range of advances in the field with 600 images that reflect the latest progress.
  • Includes new chapters—Global Scope of ACHD; Cardiac Transplantation; Electrophysiologic Abnormalities in Unoperated Patients and Residue and Sequelae After Cardiac Surgery—to provide you with the latest information on the growth of the subspecialty and its effect on treatment.
  • Presents revisions by a new authorship of experts in infectious disease, genetics and epidemiology, sports medicine, neurology, cardiac surgery, cardiac anesthesiology, and more.

Table of Contents

Section Title Page Action Price
Front Cover Cover
Congenital Heart Disease in Adults iii
Copyright Page iv
Table of Contents xi
Contributors v
Preface vii
Acknowledgments ix
SECTION I: BACKGROUND AND FACILITIES 1
CHAPTER 1. Historical Perspective 3
CHAPTER 2. National and International Scope 14
CHAPTER 3. Specialized Facilities for Adults with Congenital Heart Disease 18
FACULTY AND PATIENT POPULATION 18
CARDIAC AND NONCARDIAC CONSULTANTS 19
OUTPATIENT SERVICES 19
INPATIENT SERVICES 20
NONINVASIVE AND IMAGING LABORATORIES 20
DIAGNOSTIC AND INTERVENTIONAL CATHETERIZATION LABORATORIES 20
TRAINING, EDUCATION, AND RESEARCH 20
FUNCTIONAL CLASSIFICATIONS 21
SECTION II: SURVIVAL PATTERNS 23
CHAPTER 4. Survival Patterns Without Cardiac Surgery or Interventional Catheterization: A Narrowing Base 25
BICUSPID AORTIC VALVE 25
UNICUSPID AORTIC VALVE 27
QUADRICUSPID AORTIC VALVE 27
COARCTATION OF THE AORTA 28
FIXED SUBAORTIC STENOSIS 29
SUPRAVALVE AORTIC STENOSIS 31
EBSTEIN’S ANOMALY OF THE TRICUSPID VALVE 31
UHL’S ANOMALY 32
CONGENITALLY CORRECTED TRANSPOSITION OF THE GREAT ARTERIES (VENTRICULAR INVERSION) 32
CONGENITAL MITRAL REGURGITATION 33
PULMONARY VALVE STENOSIS 33
PULMONARY VALVE REGURGITATION 35
PULMONARY ARTERY STENOSIS 35
OSTIUM SECUNDUM ATRIAL SEPTAL DEFECT 35
IDIOPATHIC PULMONARY HYPERTENSION 37
LUTEMBACHER SYNDROME 37
SINUS VENOSUS ATRIAL SEPTAL DEFECTS 38
PARTIAL ANOMALOUS PULMONARY VENOUS CONNECTION 39
TOTAL ANOMALOUS PULMONARY VENOUS CONNECTION 40
COMMON ATRIUM 40
ATRIOVENTRICULAR SEPTAL DEFECT 40
PATENT DUCTUS ARTERIOSUS 41
VENTRICULAR SEPTAL DEFECT 42
DEFECTS IN THE INFUNDIBULAR SEPTUM 43
SINUS OF VALSALVA ANEURYSM 44
TRUNCUS ARTERIOSUS 44
COMPLETE TRANSPOSITION OF THE GREAT ARTERIES 45
DOUBLE-OUTLET VENTRICLE 45
TAUSSIG-BING ANOMALY 47
TETRALOGY OF FALLOT 47
TETRALOGY OF FALLOT WITH ABSENT PULMONARY VALVE 48
SITUS INVERSUS WITH DEXTROCARDIA 48
SITUS SOLITUS WITH DEXTROCARDIA 48
VISCERAL HETEROTAXY WITH LEFT ISOMERISM (BILATERAL LEFT-SIDEDNESS) 49
ISOLATED CONGENITAL COMPLETE HEART BLOCK 49
VENA CAVAL TO LEFT ATRIAL COMMUNICATIONS 50
CORONARY ARTERIAL FISTULA 51
ANOMALOUS ORIGIN OF THE LEFT CORONARY ARTERY FROM THE PULMONARY TRUNK 51
PULMONARY ARTERIOVENOUS FISTULAE 53
UNIVENTRICULAR HEART 54
TRICUSPID ATRESIA 55
CONGENITAL OBSTRUCTION TO LEFT ATRIAL FLOW 56
VASCULAR RINGS 56
CONGENITAL COMPLETE ABSENCE OF THE PERICARDIUM 57
CHAPTER 5. Survival Patterns After Cardiac Surgery or Interventional Catheterization: A Broadening Base 68
CONGENITALLY MALFORMED CARDIAC VALVES 68
INTRAATRIAL SURGERY 72
INTRAATRIAL SURGERY FOR COMPLEX CYANOTIC CONGENITAL HEART DISEASE 76
CENTRAL ARTERIAL SURGERY 89
SECTION III: MEDICAL CONSIDERATIONS 103
CHAPTER 6. Echocardiography in Anatomic Imaging and Hemodynamic Evaluation of Adults with Congenital Heart Disease 105
COMPREHENSIVE ANATOMIC AND HEMODYNAMIC ECHOCARDIOGRAPHY 105
DIGITAL ECHOCARDIOGRAPHY 107
VENTRICULAR FUNCTION 107
NEW AND EVOLVING ECHO-DOPPLER TECHNIQUES 108
SEGMENTAL APPROACH TO THE DIAGNOSIS OF CONGENITAL HEART DISEASE 110
SIMPLE SHUNT LESIONS 112
SPECIFIC SIMPLE SHUNT LESIONS 113
SIMPLE OBSTRUCTIVE AND REGURGITANT LESIONS 123
ISOLATED LEFT VENTRICULAR NONCOMPACTION 129
COMPLEX MALFORMATIONS 130
CHAPTER 7. Cardiac Magnetic Resonance Imaging and Computed Tomography in the Assessment of Adult Congenital Heart Disease 151
BACKGROUND 151
CLINICAL EVALUATION OF ADULT CONGENITAL HEART DISEASE 153
PHYSIOLOGIC ASSESSMENT OF FUNCTION AND FLOW 162
FUTURE OF MAGNETIC RESONANCE IMAGING AND COMPUTED TOMOGRAPHY 165
CHAPTER 8. Infective Endocarditis and Congenital Heart Disease 168
HISTORICAL PERSPECTIVE 168
EPIDEMIOLOGY 169
PATHOGENESIS 169
CONGENITAL HEART DISEASE AND INFECTIVE ENDOCARDITIS 170
DIAGNOSIS 175
COMPLICATIONS 179
TREATMENT OF ENDOCARDITIS 180
PREVENTION AND PROPHYLAXIS 185
PATIENT AND PHYSICIAN EDUCATION 189
CHAPTER 9. Management of Pregnancy and Contraception in Congenital Heart Disease 194
HISTORICAL PERSPECTIVE 194
CARDIAC DISEASE AND PREGNANCY—AN OVERVIEW 195
CARDIOVASCULAR PHYSIOLOGY DURING NORMAL PREGNANCY, LABOR, AND DELIVERY 195
CARDIAC SIGNS AND SYMPTOMS DURING PREGNANCY 197
ECHOCARDIOGRAPHY 197
PRINCIPLES OF GENERAL MANAGEMENT 197
PRECONCEPTION EVALUATION AND COUNSELING 198
HIGH-RISK CARDIAC DISEASE 199
LOW-RISK HEART DISEASE 200
DRUGS DURING PREGNANCY 200
CARDIAC SURGERY DURING PREGNANCY 201
LABOR AND DELIVERY 201
SPECIFIC CONGENITAL CARDIOVASCULAR MALFORMATIONS 203
MARFAN SYNDROME 211
PROSTHETIC HEART VALVES AND ANTICOAGULATION 212
ORAL VITAMIN K ANTAGONISTS 214
HEPARINS 215
RECOMMENDATIONS FOR ANTICOAGULATION OF MECHANICAL HEART VALVES DURING PREGNANCY 216
BENEFITS AND RISKS OF CONTRACEPTION 217
GYNECOLOGIC ENDOCRINOLOGY 218
CHAPTER 10. Genetics, Epidemiology, and Counseling 221
EPIDEMIOLOGY 221
ETIOLOGY 223
CLINICAL PRACTICE 238
CONCLUSION 242
CHAPTER 11. Exercise and Athletics in Adults with Congenital Heart Disease 248
COMPETITIVE AND RECREATIONAL ATHLETICS 248
TYPES OF EXERCISE 249
EFFECTS OF EXERCISE ON SPECIFIC TYPES OF CONGENITAL HEART DISEASE 250
CHAPTER 12. Cyanotic Congenital Heart Disease: A Multisystem Disorder 265
HEMATOLOGIC ISSUES 265
OTHER THERAPEUTIC RECOMMENDATIONS 269
OTHER HEMATOLOGIC DISORDERS 271
SYSTEMIC VASCULAR BED 274
CORONARY CIRCULATION 274
RENAL INVOLVEMENT 276
DIGITS AND LONG BONES 277
LUNGS—RESPIRATION, OXYGEN CONSUMPTION, AND VENTILATION 280
CHAPTER 13. Psychiatric and Psychosocial Disorders in Congenital Heart Disease 290
MECHANISMS OF CENTRAL NERVOUS SYSTEM INJURY IN CONGENITAL HEART DISEASE 290
PREOPERATIVE AND INTRINSIC FACTORS 290
INTRAOPERATIVE RISK FACTORS 292
EFFECTS OF SURGICAL INTERVENTION IN INFANTS AND CHILDREN WITH CONGENITAL HEART DISEASE 293
IMMEDIATE POSTOPERATIVE CONCERNS 294
SURGICAL INTERVENTION AND COGNITIVE IMPAIRMENT 294
DEVELOPMENT ACROSS THE LIFE SPAN 295
CLINICAL PSYCHIATRIC ISSUES 298
PHARMACOLOGIC TREATMENT 299
CARDIAC TRANSPLANTATION IN CHILDREN AND ADOLESCENTS 300
SUMMARY 301
CHAPTER 14. Neurologic Disorders 307
INFECTIOUS DISORDERS 307
ISCHEMIC DISORDERS 308
HEMORRHAGIC DISORDERS 315
SYNCOPE 316
HYPOXIC DISORDERS 316
SEIZURE DISORDERS 316
CONGENITAL NEUROLOGIC DISORDERS 317
NEUROLOGIC SEQUELAE OF CARDIAC SURGERY 317
PERIPHERAL MODEL OF CENTRAL NERVOUS SYSTEM NEURONAL FUNCTION 317
SECTION IV: SURGICAL CONSIDERATIONS 321
CHAPTER 15. Cardiac Surgery in Adults with Congenital Heart Disease: Operation and Reoperation 323
SYSTEMIC-TO-PULMONARY ARTERIAL SHUNTS 323
POTTS OR WATERSTON SHUNTS 323
GLENN SHUNT 324
PULMONARY ARTERIAL BANDING 324
GENERAL MANAGEMENT 324
SPECIFIC CONGENITAL MALFORMATIONS 325
CHAPTER 16. Prosthetic Materials: Selection, Use, and Long-Term Effects 342
ENDOGENOUS AUTOGRAFT BIOPROSTHETIC MATERIALS 342
EXOGENOUS BIOPROSTHETIC MATERIALS 343
SYNTHETIC MATERIALS 344
PROSTHETIC RINGS 346
MECHANICAL VALVES 346
GUIDELINES FOR CHOOSING PROSTHETIC MATERIALS 346
GUIDELINES FOR ANTICOAGULATION 347
CHAPTER 17. Cardiac Transplantation in Patients with Congenital Heart Disease 350
INDICATIONS FOR HEART TRANSPLANTATION IN PATIENTS WITH CONGENITAL HEART DISEASE 350
SPECIAL CONSIDERATIONS FOR PATIENTS WITH CONGENITAL HEART DISEASE 351
OPTIMAL IMMUNOSUPPRESSION AFTER HEART TRANSPLANTATION 354
CONCLUSION 355
CHAPTER 18. Transcatheter Interventions in Adult Congenital Heart Disease 357
INTERVENTIONS FOR SEMILUNAR VALVE AND VENTRICULAR OUTFLOW OBSTRUCTION 357
PULMONARY ARTERY STENOSIS 359
CONDUIT AND PROSTHETIC VALVE STENOSIS 360
LEFT VENTRICULAR OUTFLOW AND AORTIC VALVE OBSTRUCTION 361
EMBOLIZATION 363
OCCLUSION DEVICES 366
TRANSCATHETER VALVE PROCEDURES 371
TRANSCATHETER APPLICATIONS TO THE SINGLE VENTRICLE 374
CHAPTER 19. Noncardiac Surgery 380
GENERAL CONSIDERATIONS 380
UNOPERATED ACYANOTIC CONGENITAL HEART DISEASE 381
UNOPERATED CYANOTIC CONGENITAL HEART DISEASE 384
SURGICALLY REPAIRED CONGENITAL HEART DISEASE 386
SECTION V: RESIDUA AND SEQUELAE AFTER SURGERY OR INTERVENTIONAL CATHETERIZATION 391
CHAPTER 20. Residua and Sequelae: A Perspective 393
RESIDUA 393
SEQUELAE 401
CHAPTER 21. Residua and Sequelae Involving Cardiac Valves 407
RESIDUA 407
SEQUELAE 413
CHAPTER 22. Electrophysiologic Abnormalities: Unoperated Occurrence and Postoperative Residua and Sequelae 418
PATHOPHYSIOLOGY—MECHANISMS OF CARDIAC ARRHYTHMIAS 419
MECHANISMS OF CARDIAC ARRHYTHMIAS 419
ARRHYTHMIAS IN THE SETTING OF ACUTE MYOCARDIAL ISCHEMIA 422
RECENT ADVANCES 422
MANAGEMENT 422
FUTURE 425
MALFORMATIONS INVOLVING INTRAATRIAL SURGERY 426
MALFORMATIONS REQUIRING INTRAVENTRICULAR SURGERY 433
CONGENITAL DISEASES OF CARDIAC VALVES 440
MYOCARDIAL DISEASES 442
THERAPY FOR ARRHYTHMIAS 446
CHAPTER 23. Myocardial Growth and the Development and Regression of Increased Ventricular Mass 460
NORMAL INTRAUTERINE CARDIAC GROWTH 461
NORMAL EXTRAUTERINE CARDIAC GROWTH 463
INCREASE IN VENTRICULAR MASS BEYOND THE PROCESS OF NORMAL GROWTH 464
ULTRASTRUCTURAL RESPONSES TO OVERLOAD 466
GROSS MORPHOLOGIC AND PHYSIOLOGIC RESPONSES TO OVERLOAD 467
REGRESSION OF VENTRICULAR MASS 468
OBJECTIVES OF OPERATION 470
CONCLUSION 470
INDEX 475